Gaucher's Disease. Splenectomy

Gauchers disease presenting with portal hypertension.

Gauchers disease is a rare lysosomal storage disorder characterized by abnormal accumulation of lipid-laden macrophages in different organs. Though hepatosplenomegaly is commonly found, symptomatic presentation with portal hypertension is rare. We report a child with liver cirrhosis and bleeding esophageal varices who was diagnosed with Gaucher's disease.

Splenectomy in "big spleen disease".

Spectrum of Disease Entities in Splenectomy Specimen

Introduction: We report here our results of Pathological assessment of 35 splenectomy cases. Purpose of Study: To evaluate the subtle morphological change which is often missed due to lack of experience & knowledge. Material and Methods: It was a non-interventional descriptive study, carried out in the Pathology department of PIMS. All available splenectomy, slides were reviewed from a period o...

Partial splenectomy in sickle cell disease

Introduction: Total splenectomy in sickle cell disease is related to a high risk of fulminant sep-sis and increased incidence of other events, which have not been reported in patients with partial splenectomy. In this study we examined the patients with sickle cell disease and partial splenectomy and compared the clinical and laboratory results with non-splenectomised patients. Materials and me...

[Partial splenectomy in sickle cell disease].

INTRODUCTION Total splenectomy in sickle cell disease is related to a high risk of fulminant sepsis and increased incidence of other events, which have not been reported in patients with partial splenectomy. In this study we examined the patients with sickle cell disease and partial splenectomy and compared the clinical and laboratory results with non-splenectomized patients. MATERIAL AND MET...